| Item Type | Name |
|
Concept
|
Ventricular Flutter
|
|
Concept
|
Cytokines
|
|
Concept
|
Muscle, Smooth, Vascular
|
|
Concept
|
Enzyme-Linked Immunosorbent Assay
|
|
Concept
|
Disease Models, Animal
|
|
Concept
|
Maryland
|
|
Concept
|
Calcium Channel Blockers
|
|
Concept
|
PPAR alpha
|
|
Concept
|
Maleimides
|
|
Concept
|
Electrocardiography, Ambulatory
|
|
Concept
|
Informed Consent
|
|
Concept
|
Patient Selection
|
|
Concept
|
Magnetic Resonance Imaging, Cine
|
|
Concept
|
Transforming Growth Factor beta
|
|
Concept
|
Joint Instability
|
|
Concept
|
Serum Amyloid A Protein
|
|
Concept
|
RNA, Small Interfering
|
|
Concept
|
Bone Development
|
|
Concept
|
Kaplan-Meier Estimate
|
|
Concept
|
Cell Lineage
|
|
Concept
|
Ankyrins
|
|
Concept
|
Animals, Newborn
|
|
Concept
|
Receptor, Angiotensin, Type 2
|
|
Concept
|
Mitochondria
|
|
Concept
|
Simethicone
|
|
Concept
|
Endocardium
|
|
Concept
|
Incidence
|
|
Concept
|
Heart Block
|
|
Concept
|
Proportional Hazards Models
|
|
Concept
|
Recurrence
|
|
Concept
|
Postmortem Changes
|
|
Concept
|
Morbidity
|
|
Concept
|
Ion Channels
|
|
Concept
|
Marfan Syndrome
|
|
Concept
|
Magnetic Resonance Imaging
|
|
Concept
|
Actins
|
|
Concept
|
Receptors, Transforming Growth Factor beta
|
|
Concept
|
Membrane Potentials
|
|
Concept
|
Rare Diseases
|
|
Concept
|
Canada
|
|
Concept
|
Pyrazoles
|
|
Concept
|
Loeys-Dietz Syndrome
|
|
Concept
|
Disease Progression
|
|
Concept
|
Desmogleins
|
|
Concept
|
Cadherins
|
|
Concept
|
Sensitivity and Specificity
|
|
Concept
|
Death, Sudden, Cardiac
|
|
Concept
|
Aorta, Thoracic
|
|
Concept
|
Anthracyclines
|
|
Concept
|
Myopathies, Structural, Congenital
|
|
Concept
|
Single-Blind Method
|
|
Concept
|
Registries
|
|
Concept
|
Treatment Outcome
|
|
Concept
|
Clinical Trials, Phase III as Topic
|
|
Concept
|
Child Development
|
|
Concept
|
NIH 3T3 Cells
|
|
Concept
|
Protein Kinase Inhibitors
|
|
Concept
|
Genetic Testing
|
|
Concept
|
Confidence Intervals
|
|
Concept
|
Amino Acid Substitution
|
|
Concept
|
Myosin Heavy Chains
|
|
Concept
|
Animals
|
|
Concept
|
Chi-Square Distribution
|
|
Concept
|
Interviews as Topic
|
|
Concept
|
Syndrome
|
|
Concept
|
Feasibility Studies
|
|
Concept
|
Mitogen-Activated Protein Kinase 1
|
|
Concept
|
Chronic Disease
|
|
Concept
|
Adrenergic beta-Antagonists
|
|
Concept
|
Electrophysiology
|
|
Concept
|
Societies, Medical
|
|
Concept
|
Magnetic Resonance Angiography
|
|
Concept
|
Double-Blind Method
|
|
Concept
|
Statistics as Topic
|
|
Concept
|
Amino Acid Sequence
|
|
Concept
|
Disease-Free Survival
|
|
Concept
|
Mice, Knockout
|
|
Concept
|
Vasodilator Agents
|
|
Concept
|
Cohort Studies
|
|
Concept
|
Nuclear Envelope
|
|
Concept
|
Antibodies
|
|
Concept
|
Boston
|
|
Concept
|
Antineoplastic Agents
|
|
Concept
|
Natriuretic Peptide, Brain
|
|
Concept
|
Coronary Artery Disease
|
|
Concept
|
Myocytes, Cardiac
|
|
Concept
|
Multilevel Analysis
|
|
Concept
|
Desmoplakins
|
|
Concept
|
Mortality
|
|
Concept
|
Calcium
|
|
Concept
|
Platelet Factor 4
|
|
Concept
|
Clinical Trials, Phase II as Topic
|
|
Concept
|
Chromosomes, Human, Pair 4
|
|
Concept
|
Acute Disease
|
|
Concept
|
Propranolol
|
|
Concept
|
Pancreatic Neoplasms
|
|
Concept
|
Sarcomeres
|
|
Concept
|
Smad2 Protein
|
|
Concept
|
Preconception Care
|
|
Concept
|
Myocardial Infarction
|
|
Concept
|
Genetics, Medical
|
|
Concept
|
Genetic Predisposition to Disease
|
|
Concept
|
Syncope
|
|
Concept
|
Muscular Dystrophy, Emery-Dreifuss
|
|
Concept
|
Disease Management
|
|
Concept
|
Microfibrils
|
|
Concept
|
Observer Variation
|
|
Concept
|
Biopsy
|
|
Concept
|
Myocardium
|
|
Concept
|
Pregnancy Complications, Cardiovascular
|
|
Concept
|
Head and Neck Neoplasms
|
|
Concept
|
Amyloid
|
|
Concept
|
Logistic Models
|
|
Concept
|
Connexin 43
|
|
Concept
|
Mice
|
|
Concept
|
Contrast Media
|
|
Concept
|
Cardiovascular Agents
|
|
Concept
|
Arrhythmias, Cardiac
|
|
Concept
|
Clinical Trials as Topic
|
|
Concept
|
Mesoderm
|
|
Concept
|
Sodium
|
|
Concept
|
DNA Primers
|
|
Concept
|
Immunoglobulin kappa-Chains
|
|
Concept
|
Diastole
|
|
Concept
|
Emergency Service, Hospital
|
|
Concept
|
Ventricular Fibrillation
|
|
Concept
|
Early Termination of Clinical Trials
|
|
Concept
|
Barth Syndrome
|
|
Concept
|
Linear Models
|
|
Concept
|
Mitogen-Activated Protein Kinase 3
|
|
Concept
|
Microscopy, Confocal
|
|
Concept
|
Fat Necrosis
|
|
Concept
|
Angiotensin II Type 1 Receptor Blockers
|
|
Concept
|
Aortic Aneurysm
|
|
Concept
|
Antihypertensive Agents
|
|
Concept
|
Live Birth
|
|
Concept
|
Melanoma
|
|
Concept
|
Mitral Valve Prolapse
|
|
Concept
|
Matrix Metalloproteinase 9
|
|
Concept
|
Patch-Clamp Techniques
|
|
Concept
|
Sodium Channels
|
|
Concept
|
Matrix Metalloproteinase 2
|
|
Concept
|
Mice, Inbred C57BL
|
|
Concept
|
RNA, Transfer, Leu
|
|
Concept
|
Bone Morphogenetic Proteins
|
|
Concept
|
Polycystic Kidney, Autosomal Dominant
|
|
Concept
|
Sarcoidosis
|
|
Concept
|
Retrospective Studies
|
|
Concept
|
Models, Statistical
|
|
Concept
|
Isolated Noncompaction of the Ventricular Myocardium
|
|
Concept
|
Mice, Transgenic
|
|
Concept
|
Aortic Rupture
|
|
Concept
|
Zebrafish Proteins
|
|
Concept
|
Multivariate Analysis
|
|
Concept
|
Mitogen-Activated Protein Kinase 14
|
|
Concept
|
Quality of Life
|
|
Concept
|
Antigens, CD
|
|
Concept
|
Gastrointestinal Hemorrhage
|
|
Concept
|
Professional-Family Relations
|
|
Concept
|
Cicatrix
|
|
Concept
|
Mole Rats
|
|
Concept
|
Heart Rate
|
|
Concept
|
Hospitalization
|
|
Concept
|
Hydralazine
|
|
Concept
|
RNA Splice Sites
|
|
Concept
|
Severity of Illness Index
|
|
Concept
|
RNA, Messenger
|
|
Concept
|
Survival Rate
|
|
Concept
|
Expert Testimony
|
|
Concept
|
MAP Kinase Signaling System
|
|
Concept
|
Humans
|
|
Concept
|
Heart
|
|
Concept
|
Likelihood Functions
|
|
Concept
|
Pericardium
|
|
Concept
|
Desmocollins
|
|
Concept
|
Cell Movement
|
|
Concept
|
Heart Conduction System
|
|
Concept
|
beta Catenin
|
|
Concept
|
Receptor, Angiotensin, Type 1
|
|
Concept
|
Europe
|
|
Concept
|
Chromosomes, Human, Pair 15
|
|
Concept
|
Adaptor Proteins, Signal Transducing
|
|
Concept
|
Dystrophin
|
|
Concept
|
Longitudinal Studies
|
|
Concept
|
TRPP Cation Channels
|
|
Concept
|
Calpain
|
|
Concept
|
Heart-Assist Devices
|
|
Concept
|
Mitogen-Activated Protein Kinase 8
|
|
Concept
|
Fatal Outcome
|
|
Concept
|
Inflammation
|
|
Concept
|
Cause of Death
|
|
Concept
|
American Heart Association
|
|
Concept
|
Genes, Mitochondrial
|
|
Concept
|
Giant Cells
|
|
Concept
|
Aorta
|
|
Concept
|
Neutralization Tests
|
|
Concept
|
Microsatellite Repeats
|
|
Concept
|
alpha-Galactosidase
|
|
Concept
|
Atrial Fibrillation
|
|
Concept
|
Muscular Dystrophy, Duchenne
|
|
Concept
|
Glucagonoma
|
|
Concept
|
Survival Analysis
|
|
Concept
|
Systole
|
|
Concept
|
Angiotensin II
|
|
Concept
|
Analysis of Variance
|
|
Concept
|
Reverse Transcriptase Polymerase Chain Reaction
|
|
Concept
|
Benzoates
|
|
Concept
|
Troponin T
|
|
Concept
|
Smad4 Protein
|
|
Concept
|
Amyloidosis
|
|
Concept
|
Anti-Arrhythmia Agents
|
|
Concept
|
Protein Structure, Quaternary
|
|
Concept
|
Diuretics
|
|
Concept
|
Action Potentials
|
|
Concept
|
Desmoglein 3
|
|
Concept
|
Interferon-alpha
|
|
Concept
|
Friedreich Ataxia
|
|
Concept
|
Angiotensin-Converting Enzyme Inhibitors
|
|
Concept
|
Netherlands
|
|
Concept
|
Genetic Counseling
|
|
Concept
|
Physical Endurance
|
|
Concept
|
Mass Screening
|
|
Concept
|
Cardiomyopathy, Hypertrophic, Familial
|
|
Concept
|
Ehlers-Danlos Syndrome
|
|
Concept
|
Graft Rejection
|
|
Concept
|
Prevalence
|
|
Concept
|
Case-Control Studies
|
|
Concept
|
Monoclonal Gammopathy of Undetermined Significance
|
|
Concept
|
Induced Pluripotent Stem Cells
|
|
Concept
|
Microfilament Proteins
|
|
Concept
|
Aortic Aneurysm, Thoracic
|
|
Concept
|
Predictive Value of Tests
|
|
Concept
|
Reproducibility of Results
|
|
Concept
|
Baltimore
|
|
Concept
|
Prospective Studies
|
|
Concept
|
Fabry Disease
|
|
Concept
|
Amyloid Neuropathies, Familial
|
|
Concept
|
Stem Cell Transplantation
|
|
Concept
|
Cross-Sectional Studies
|
|
Concept
|
Activin Receptors, Type I
|
|
Concept
|
Mitral Valve
|
|
Concept
|
Biphenyl Compounds
|
|
Concept
|
Codon, Nonsense
|
|
Concept
|
Infant, Newborn
|
|
Concept
|
Randomized Controlled Trials as Topic
|
|
Concept
|
Progeria
|
|
Concept
|
Genome-Wide Association Study
|
|
Concept
|
Losartan
|
|
Concept
|
Cesarean Section
|
|
Concept
|
Surveys and Questionnaires
|
|
Concept
|
Fibrosis
|
|
Concept
|
Enzyme Inhibitors
|
|
Concept
|
Rats, Wistar
|
|
Concept
|
Myotonic Dystrophy
|
|
Concept
|
Glucocorticoids
|
|
Concept
|
Heart Ventricles
|
|
Concept
|
Point Mutation
|
|
Concept
|
Nicotinic Acids
|
|
Concept
|
Lymphatic Metastasis
|
|
Concept
|
Muscular Dystrophies, Limb-Girdle
|
|
Concept
|
Desmoglein 2
|
|
Concept
|
Greece
|
|
Concept
|
Polymerase Chain Reaction
|
|
Concept
|
Indazoles
|
|
Concept
|
United States
|
|
Concept
|
Polyploidy
|
|
Concept
|
Sulfonamides
|
|
Concept
|
Myocardial Contraction
|
|
Concept
|
Gene Deletion
|
|
Concept
|
Epicardial Mapping
|
|
Concept
|
Risk Assessment
|
|
Concept
|
Skin Neoplasms
|
|
Concept
|
In Situ Hybridization, Fluorescence
|
|
Concept
|
Tachycardia, Ventricular
|
|
Concept
|
Cardiac Myosins
|
|
Concept
|
Mutation, Missense
|
|
Concept
|
Risk
|
|
Concept
|
Lamin Type A
|
|
Concept
|
Risk Factors
|
|
Concept
|
Immunoglobulin lambda-Chains
|
|
Concept
|
Tachycardia, Sinus
|
|
Concept
|
gamma Catenin
|
|
Concept
|
Sweden
|
|
Concept
|
Base Sequence
|
|
Concept
|
Follow-Up Studies
|
|
Concept
|
Zebrafish
|
|
Concept
|
Siblings
|
|
Concept
|
Immunohistochemistry
|
|
Concept
|
Mice, Mutant Strains
|
|
Concept
|
Anthracenes
|
|
Concept
|
Rats, Transgenic
|
|
Concept
|
Mouth Mucosa
|
|
Concept
|
Age Distribution
|
|
Concept
|
Troponin I
|
|
Academic Article
|
Losartan, an AT1 antagonist, prevents aortic aneurysm in a mouse model of Marfan syndrome.
|
|
Academic Article
|
Impact of genotype on clinical course in arrhythmogenic right ventricular dysplasia/cardiomyopathy-associated mutation carriers.
|
|
Academic Article
|
Cardiac transplantation in arrhythmogenic right ventricular dysplasia/cardiomyopathy.
|
|
Academic Article
|
Tafamidis in transthyretin amyloid cardiomyopathy: effects on transthyretin stabilization and clinical outcomes.
|
|
Academic Article
|
Genetic evaluation of familial cardiomyopathy.
|
|
Academic Article
|
Neonatal Transplantation Confers Maturation of PSC-Derived Cardiomyocytes Conducive to Modeling Cardiomyopathy.
|
|
Academic Article
|
Characterization of microsatellite markers flanking FBN1: utility in the diagnostic evaluation for Marfan syndrome.
|
|
Academic Article
|
Fluctuating creatinine in the cardiac unit.
|
|
Academic Article
|
Outcomes of catheter ablation of ventricular tachycardia in arrhythmogenic right ventricular dysplasia/cardiomyopathy.
|
|
Academic Article
|
Use of genetics in the clinical evaluation and management of heart failure.
|
|
Academic Article
|
Reader- and instrument-dependent variability in the electrocardiographic assessment of arrhythmogenic right ventricular dysplasia/cardiomyopathy.
|
|
Academic Article
|
Cutaneous nerve biomarkers in transthyretin familial amyloid polyneuropathy.
|
|
Academic Article
|
Morphologic variants of familial arrhythmogenic right ventricular dysplasia/cardiomyopathy a genetics-magnetic resonance imaging correlation study.
|
|
Academic Article
|
The Role of Genetics in Peripartum Cardiomyopathy.
|
|
Academic Article
|
Loss of elastic fiber integrity and reduction of vascular smooth muscle contraction resulting from the upregulated activities of matrix metalloproteinase-2 and -9 in the thoracic aortic aneurysm in Marfan syndrome.
|
|
Academic Article
|
Long-term efficacy of catheter ablation of ventricular tachycardia in patients with arrhythmogenic right ventricular dysplasia/cardiomyopathy.
|
|
Academic Article
|
Lack of Relationship Between Serum Cardiac Troponin I Level and Giant Cell Myocarditis Diagnosis and Outcomes.
|
|
Academic Article
|
Therapy of Marfan syndrome.
|
|
Academic Article
|
Sildenafil does not improve cardiomyopathy in Duchenne/Becker muscular dystrophy.
|
|
Academic Article
|
Distinguishing arrhythmogenic right ventricular cardiomyopathy/dysplasia-associated mutations from background genetic noise.
|
|
Academic Article
|
Comprehensive Versus Targeted Genetic Testing in Children with Hypertrophic Cardiomyopathy.
|
|
Academic Article
|
Reversible cardiomyopathy caused by administration of interferon alpha.
|
|
Academic Article
|
Familial hypertrophic cardiomyopathy associated with cardiac beta-myosin heavy chain and troponin I mutations.
|
|
Academic Article
|
Incidence and predictors of implantable cardioverter-defibrillator therapy in patients with arrhythmogenic right ventricular dysplasia/cardiomyopathy undergoing implantable cardioverter-defibrillator implantation for primary prevention.
|
|
Academic Article
|
Risk stratification in arrhythmogenic right ventricular dysplasia/cardiomyopathy-associated desmosomal mutation carriers.
|
|
Academic Article
|
Arrhythmogenic Right Ventricular Dysplasia/Cardiomyopathy in the Pediatric?Population: Clinical Characterization and Comparison With?Adult-Onset?Disease.
|
|
Academic Article
|
Regional Variation in RBM20 Causes a Highly Penetrant Arrhythmogenic Cardiomyopathy.
|
|
Academic Article
|
FLNC truncations cause arrhythmogenic right ventricular cardiomyopathy.
|
|
Academic Article
|
Exercise triggers CAPN1-mediated AIF truncation, inducing myocyte cell death in arrhythmogenic cardiomyopathy.
|
|
Academic Article
|
Influence of Panel Selection on Yield of Clinically Useful Variants in Arrhythmogenic Right Ventricular Cardiomyopathy Families.
|
|
Concept
|
Cardiac Resynchronization Therapy
|
|
Concept
|
Walk Test
|
|
Concept
|
Laser Capture Microdissection
|
|
Concept
|
NAV1.5 Voltage-Gated Sodium Channel
|
|
Concept
|
NAV1.8 Voltage-Gated Sodium Channel
|
|
Concept
|
Connectin
|
|
Concept
|
Filamins
|
|
Concept
|
Vascular Remodeling
|
|
Concept
|
Clinical Decision-Making
|
|
Concept
|
Sildenafil Citrate
|
|
Concept
|
Serotonin and Noradrenaline Reuptake Inhibitors
|
|
Concept
|
Loss of Function Mutation
|
|
Concept
|
Fibrillin-1
|
|
Concept
|
Protein Domains
|
|
Concept
|
Mice, 129 Strain
|
|
Concept
|
Haploinsufficiency
|
|
Concept
|
Angiotensin Receptor Antagonists
|